INTRODUCTION

Glomus tumors are uncommon, encapsulated, slowly growing, highly vascular, and locally invasive tumors. They are included in a group of tumors referred to as paragangliomas, which occur at various sites and include carotid body,
glomus vagale, and glomus tympanicum tumors in head and neck.
Based on the presence of catecholamines and neuropeptides, paraganglia are included in the amine precursor uptake and decarboxylase (APUD) system, which has more recently been referred to as the diffuse neuroendocrine system (DNES). Although most paragangliomas are sporadic, they can be familial with autosomal dominant inheritance and incomplete penetrance.